Left paranasal hemophilic pseudotumor in a 5-year-old boy: A case report


Submitted: June 30, 2019
Accepted: January 7, 2020
Published: January 15, 2020
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Authors

  • Saleh Yuguda Department of Hematology and Blood Transfusion, Gombe State University/Federal Teaching Hospital Gombe, Gombe State, Nigeria.
  • Ahmed Iya Girei Department of Hematology and Blood Transfusion, Gombe State University/Federal Teaching Hospital Gombe, Gombe State, Nigeria.
  • Rufai Abdu Dachi Department of Hematology and Blood Transfusion, Abubakar Tafawa Balewa University Teaching Hospital/Abubakar Tafawa Balewa University Bauchi, Bauchi State, Nigeria.
  • Sani Adamu Department of Surgery, Pediatric Surgery Unit, Gombe State University/Federal Teaching Hospital Gombe, Gombe State, Nigeria.

Hemophilic pseudotumors are rare complications of hemophilia that are seen in 1-2% of patients commonly affecting patients with severe disease. Hemophilic pseudotumors occur as a result of recurrent poorly managed or untreated bleeding either in the soft tissue or bone. We report a 5-year-old boy with a previously undiagnosed hemophilia A who developed left paranasal swelling following a fall from a height. He was diagnosed with hemophilic pseudotumor and successfully managed conservatively with factor VIII replacement.


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